Superior Semicircular Canal Dehiscence Syndrome Presenting with Sudden Deafness and Vertigo after Trauma / 대한평형의학회지

Superior semicircular canal dehiscence syndrome (SCDS) is characterized by cochleovestibular hyper-responsiveness symptoms including sound- and pressure-evoked vertigo and oscillopsia, autophony, hyperacusis and ear fullness. The typical audiometric feature of SCDS is known as conductive hearing loss at low frequency. A 43-year-old man presented with unilateral sudden deafness after several events of heading during soccer game. High-resolution temporal bone computed tomography revealed a dehiscence of superior canal encased by superior petrous sinus. We reviewed audio-vestibular findings in this patient and speculated potential pathogenic mechanisms of sudden deafness in SCDS with literature review.

Superior Semicircular Canal Dehiscence Syndrome / 대한이비인후과학회지

Superior canal dehiscence (SCD) syndrome is characterized by sound and pressure induced vertigo accompanying vertical-torsional nystagmus. Since the severity of symptoms and signs in SCD may depend on the amount of bony dehiscence of the superior semicircular canal, typical clinical presentations are not always accompanied in every patient. And symptoms of SCD are frequently vague and non-specific, such as aural fullness, disequilibrium or floating sensation of dizziness. Routine vestibular laboratory tests cannot provide disease-specific diagnostic clue, which makes this diagnosis more difficult. This review provides information to understand the pathophysiologic mechanism of symptoms and signs in SCD, and characteristic features of diagnostic tests targeted to SCD.

A Case of Superior Canal Dehiscence Syndrome as a Cause of Step-Synchronous Tinnitus / 대한이비인후과학회지

The superior canal dehiscence syndrome (SCDS) is a rare disorder caused by the dehiscence of the temporal bone overlying the superior semicircular canal. It has become apparent that SCDS can lead to a variety of clinical manifestations, vestibular and/or auditory, in contrast to the typical symptoms, as initially described. We recently examined a 54-year-old woman with unilateral stepsynchronous tinnitus without any vestibular symptoms. Tinnitus is a quite unremarkable finding among variable symptoms of the syndrome; however, it can be one of the clues to identify SCDS when it is accompanied by low-frequency conductive hearing loss. Therefore, in diagnosing SCDS, attention must be also paid to those patients with nonspecific complaints, for example, stepsynchronous tinnitus.